本文選題：副腫瘤性天皰瘡 + 巨淋巴結增生��； 參考：《臨床皮膚科雜志》2017年03期

【摘要】：報告1例副腫瘤天皰瘡并發(fā)兒童型Castleman病。患者男,15歲。黏膜糜爛5個月余,全身紅斑、水皰伴發(fā)熱4個月。皮膚科檢查:全身皮膚泛發(fā)紅斑、斑丘疹,大小不一的厚壁水皰,不易破潰,尼氏征陰性。黏膜糜爛、潰瘍,表面附著膿性分泌物。皮損組織病理及間接免疫熒光支持副腫瘤性天皰瘡診斷,盆腔CT提示左側髂外動脈、閉孔旁單發(fā)結節(jié)和腫物,切除腫物經組織病理證實為Castleman病。術后15 d患者死于感染性休克。
[Abstract]:A case of paraneoplastic pemphigus complicated with childhood Castleman disease was reported. The patient was 15 years old. Mucosal erosion more than 5 months, systemic erythema, blister with fever for 4 months. Dermatology examination: systemic skin erythema, macular papules, different sizes of thick blisters, not easy to break, Nissl sign negative. Mucosal erosion, ulcer, surface attachment purulent secretion. The diagnosis of paraneoplastic pemphigus was supported by histopathology and indirect immunofluorescence. Pelvic CT revealed left external iliac artery, solitary nodules and masses adjacent to obturator, and Castleman's disease was confirmed by histopathology. The patients died of septic shock 15 days after operation.
【作者單位】： 中國中醫(yī)科學院廣安門醫(yī)院皮膚科;
【分類號】：R73;R758.66

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相關期刊論文 前5條

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本文編號：2095419