兒童腎透明細(xì)胞肉瘤的多學(xué)科診治與隨訪
發(fā)布時(shí)間:2018-04-23 14:57
本文選題:腎透明細(xì)胞肉瘤 + 兒童。 參考:《上海交通大學(xué)學(xué)報(bào)(醫(yī)學(xué)版)》2017年02期
【摘要】:目的·探討兒童腎透明細(xì)胞肉瘤的臨床特點(diǎn)與多學(xué)科聯(lián)合治療。方法·收集2011年1月—2016年1月上海交通大學(xué)醫(yī)學(xué)院附屬新華醫(yī)院收治的7例腎透明細(xì)胞肉瘤患兒的資料,對(duì)臨床表現(xiàn)、影像學(xué)和病理學(xué)特點(diǎn)及治療和隨訪情況等進(jìn)行回顧性分析。結(jié)果·7例患兒中,男6例,女1例;中位年齡為28個(gè)月(4~59個(gè)月);I期3例,Ⅲ期2例,Ⅳ期2例。經(jīng)小兒血液/腫瘤科、兒外科、病理科、放射科與放療科等多學(xué)科討論和評(píng)估后,納入CCCG-WT-2009方案治療。中位隨訪時(shí)間為22個(gè)月(8~56)個(gè)月;6例存活,1例死亡。結(jié)論·多學(xué)科聯(lián)合診治模式能有效改善兒童腎透明細(xì)胞肉瘤的預(yù)后,CCCG-WT-2009方案對(duì)早期兒童腎透明細(xì)胞肉瘤的治療效果好,治愈率高;晚期兒童腎透明細(xì)胞肉瘤的治療有待進(jìn)一步探討和完善。
[Abstract]:Objective to investigate the clinical features and multi-disciplinary treatment of renal hyaline cell sarcoma in children. Methods from January 2011 to January 2016, 7 cases of renal clear cell sarcoma were collected from Xinhua Hospital affiliated to Shanghai Jiaotong University Medical College. The imaging and pathological features, treatment and follow-up were retrospectively analyzed. Results among the 7 cases, 6 were male and 1 female, with a median age of 28 months (4 ~ 59 months), 3 cases with stage I, 2 cases with stage 鈪,
本文編號(hào):1792442
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